DNAJB9: Demystifying Fibrillary Glomerulonephritis

Fibrillary glomerulonephritis (GN) is a rare disease which accounts for about 1% of all kidney biopsies. The very first description of the disease was published by Rosenmann and Eliakim in 1977. They described a patient with nephrotic syndrome due to deposition of what they describe as “an amyloid-like material in the glomeruli,” but upon ultrastructural analysis, this material “appeared shorter than amyloid fibrils”

Post by NSMC2019 Intern and Nephrology Fellow - Lovy Gaur

Link to original post on Renal Fellow Network